Dysembryoplastic neuroepithelial tumor (DNET) is relatively uncommon benign tumor, responsible for causing partial seizures in children, many of those cases may be medically refractory.
The most common location is temporal lobe, as in this case (about 65% of cases). About 20% cases involve frontal lobe. The remainder of cases involve caudate nucleus, cerebellum and pons.
The tumor can be easily diagnosed with the help of MRI. On FLAIR images, the lesion has mixed signal intensities with bright rim sign. Calcification may be noted. On T1W post contrast, enhancement is seen in 20-30% cases.
This 16-year old child presented with recurrent seizures of two years duration, which was inadequately controlled on medications. He was referred for surgery.
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